Coarctation of the aorta is a relatively common defect that accounts for 5-8% of all congenital heart defects and is characterized by discrete medial thickening with superimposed neointimal tissue, leading to aortic lumen narrowing of different degrees.
Today’s knowledge is that the majority of lesions are juxtaductal, with the classic coarctation located in the thoracic aorta distal to the origin of the left subclavian artery at about the level of the ductal structure . However, a coarcted segment may be present in the distal descending thoracic or abdominal aorta and is referred as Middle Aortic Syndrome (MAS). This entity is extremely rare, representing only 0.5-2% of all aortic coarctation cases , with total number of published patients not exceeding three hundred. Congenital, acquired, inflammatory, and infectious etiologies have been proposed.
Published on: Oct 16, 2015 Pages: 13-16